Tuesday, 22 October 2013

Von wilibrand disease

Autosomal dominant

Mc hereditary bleeding disordr

Platlet adhesion defect

Prolonged bt,aptt

Decrease factor 8 may b mod reduced

3 types
Type 1-- partial redctn in vwf
Typ 2-- abnorml form vwf
Typ3-- total lack vwf

defctv platlet aggregation with ristocetin

Rx factor 8 cryoppt

Additional fact ::hemarthrosis
N muscle hematoma z rare
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